Ramsay Hunt syndrome is a painful rash around the ear that occurs when the varicella zostervirus infects a nerve in the head.
The varicella zoster virus that causes Ramsay Hunt syndrome is the same virus that causes chickenpox and shingles.
In people with Ramsay Hunt syndrome, the virus is believed to infect the facial nerve near the inner ear. This leads to irritation and swelling of the nerve.
Exams and Tests
- Painful rash on the eardrum, ear canal, earlobe, tongue, and roof of the mouth on the side where there is weakness of the face
- Hearing loss on one side
- Sensation of things spinning (vertigo)
- Weakness on one side of the face that causes difficulty closing one eye, eating (food falls out of the weak corner of the mouth), making expressions, and making fine movements of the face, as well as facial droop and paralysis on one side of the face
A doctor will usually diagnose Ramsay Hunt Syndrome by looking for signs of weakness in the face and a blister-like rash.
Tests may include:
- Blood tests for varicella zoster virus
- Electromyography (EMG)
- Lumbar puncture
- MRI of the head
- Nerve conduction (to determine the amount of damage to the facial nerve)
- Skin tests for varicella zoster virus
Strong anti-inflammatory drugs called steroids (such as prednisone) are usually prescribed for 5 - 7 days. Antiviral medications, such as acyclovir or valacyclovir, can be given for 7 - 10 days, although the benefit of antiviral medications is uncertain.
Sometimes strong painkillers are also needed if the pain continues even with steroids. While you have weakness of the face, wear an eye patch to prevent injury to the cornea (corneal abrasion) and other damage to the eye if the eye does not close completely. Some people may use a special eye lubricant at night and artificial tears during the day to prevent the eye from drying out.
If you have dizziness, your doctor can recommend other medications.
The more severe the damage, the longer it will take to recover, and the lower the chance that you will completely regain normal function. If there is not much damage to the nerve, you should get better completely within a few weeks. If damage is more severe, you may not fully recover, even after several months.
Overall, your chances of recovery are better if the treatment is started within 3 days after the symptoms begin. When treatment is started within this time, 70% of patients make a full recovery.
However, when the treatment is delayed for more than 3 days, the chances of a complete recovery drop to about 50%. Children are more likely to have a complete recovery than adults.
Recovery may be complicated if the nerve grows back to the wrong areas. When this happens, inappropriate responses, such as tears when laughing or chewing may occur. Other people may experience blinking of the eye when they talk or chew food.
Source: NIH MedlinePlus